Categories Examples Humoral (antibody) deficiencies X-linked agammaglobulinemia (XLA) Common variable immunodeficiencies (CVID) Hyper-IgM syndromes Combined immunodeficiencies Severe combined immunodeficiencies (SCID) Complete DiGeorge syndrome Phagocytic defects Severe congenital neutropenia (SCN) Chronic…
Fig. 42.1 Purpuric papules over the tip of the toes in a 9-year-old girl Complete blood count, prothrombin time, partial thromboplastin time, and fibrinogen level were within normal limits. The…
Fig. 33.1 Palpable purpura over the left leg of a 10-year-old boy with IgAV/HSP This patient is a typical example of a child with severe IgA vasculitis (IgAV; formerly Henoch-Schönlein…
Fig. 32.1 Calcinotic nodules in a child with juvenile dermatomyositis At the end of 6-year follow-up, her muscle weakness was in remission for >2 years, and methotrexate could be completely…
Fig. 21.1 Sweling around lateral malleolus of right ankle with MRI of the region and ulcreated positive Mantoux test. (a) The arrow shows swelling and erythema around the lateral malleolus….
Disease status Parameters to be fulfilled per the JIA subcategory Inactive disease No active arthritis No fever, rash, serositis, splenomegaly, or generalized lymphadenopathy attributable to JIA No active uveitis Normal…
Pediatric Adult Triadic or family consultation Dyadic or individual consultation Assumes patient dependence Assumes patient independence Multidisciplinary team Limited multidisciplinary team Consultation time longer Consultation time shorter Procedural pain management…
© Springer Science+Business Media Singapore 2017Sujata Sawhney and Amita Aggarwal (eds.)Pediatric Rheumatology10.1007/978-981-10-1750-6_8 8. Biologic Response Modifiers in Pediatric Rheumatology Alessandro Consolaro1 and Nicola Ruperto2 (1) Istituto Giannina Gaslini, University of Genova and Second Division of Pediatrics, Genova,…
Drug Dose (mg/kg/day unless otherwise noted) Maximal dose (mg/day) Doses per day Remarks Acetylsalicylic acid (ASA) 80–100 (<25 kg); 2500 mg/m2 (>25 kg) Antiplatelet dose 3–5 mg/kg/day single dose 4900…
Fig. 1.1 An example of recent advances in pediatric rheumatology (From Infevers: an online database for autoinflammatory mutations. Copyright. Available at http://fmf.igh.cnrs.fr/ISSAID/infevers/. Accessed April 13, 2016) That indeed is progress….
