Clinodactyly
Robert Carrigan
DEFINITION
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Clinodactyly refers to an abnormal about of radioulnar angulation of a digit (>15 degrees).
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The small finger is most commonly observed.
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This condition is often bilateral.
ANATOMY
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The finger consists of three phalanges (proximal, middle, and distal).
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The normal phalangeal physis is located at the proximal portion of each phalanx.
PATHOGENESIS
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The angulation is result of abnormal development of one of the phalanges (most often the middle phalanx [p2]).
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Abnormal development of the phalanx may be due to an irregular physis (longitudinal bracket epiphysis). This may also be referred to as a delta phalanx.
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The tethering effect of the bracket epiphysis on the radial side of the finger causes abnormal growth of the phalanx resulting in a triangular or trapezoidal shape.
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Extra bones may be encountered.
NATURAL HISTORY
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The natural history of clinodactyly is variable and poorly documented, owing to the great number of cases that are asymptomatic and do not require treatment.
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Angulation may be stable or rapidly progressive at times of growth, depending on the extent of the involvement of the physis and/or presence of extra phalanges.
PATIENT HISTORY AND PHYSICAL EXAM FINDINGS
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Clinodactyly may be present at birth or develop during a period of growth (FIG 1).
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Clinodactyly is often bilateral in the small finger.
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Clinodactyly is an autosomal dominant condition with variable penetration.
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Involvement of the thumb is rare and is associated with varying syndromes.
IMAGING AND OTHER DIAGNOSTIC STUDIES
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Standard radiographs (three views: anteroposterior[AP], lateral [LAT], and oblique [OBL]) of the hand and affected digit are sufficient to determine the area of involvement.
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Contralateral images are useful for comparison.
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Advanced imaging such as computed tomography (CT) is rarely needed. Magnetic resonance imaging (MRI) may be useful to delineate the shape of a bracket diaphysis.
DIFFERENTIAL DIAGNOSIS
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The diagnosis of clinodactyly is straightforward; clinical examination and radiographs are sufficient to make the diagnosis.
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Associated syndrome should be screened for, these include Down, Rubinstein-Taybi, Apert, and Russell-Silver.
NONOPERATIVE MANAGEMENT
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Observation may be considered for angulated digits that do not impair function. Splinting is not effective.
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Most cases can be treated nonoperatively; surgery should be considered for significant angular deformity that compromises hand function.
SURGICAL MANAGEMENT
Preoperative Planning
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Timing of surgery is variable, depending on the degree of angulation and how much growth potential remains.
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Small amounts of angulation with little remaining growth potential may be addressed when the child is older.
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Larger amounts of angulation or children with the potential for worsening angulation may consider earlier intervention.
Positioning
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The patient is positioned supine on the operating room table and the body is pulled over to the affected side.FIG 1 • Clinodactyly of the index finger from osteochondroma in a child with multiple hereditary exostosis.
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